Abstract
Hemangioblastomas account for approximately 1.5% to 2.5% of all central nervous system tumors and 7% to 8% of all posterior fossa tumors, but are the most common primary tumor of the cerebellar hemisphere. The majority of posterior fossa hemangioblastomas involve the cerebellar hemispheres (70%), but other locations include the brainstem (24%), cerebellopontine angle (2%), fourth ventricle (2%), and craniocervical junction (2%). Single tumors may appear sporadically, whereas patients with multiple tumors typically have von Hippel-Lindau disease. Patients can present with symptoms of elevated intracranial pressure, including headaches, nausea, and vomiting, as well as cerebellar symptoms. Surgical resection is the standard of care, but surgery can be associated with significant morbidity, including cranial nerve deficits, postoperative hemorrhage, hydrocephalus, pseudomeningocele, meningitis, and pneumonia, among others. In this chapter, we present a case of a patient with a right cerebellar hemisphere hemangioblastoma.